64-Slice MDCT imaging of endocardial cushion defect associated with other cardiac and extracardiac abnormalities

Oyama, Noriko; Goto, Daisuke; Sasaki, Tsukasa; Tsutsui, Hiroyuki; Tamaki, Nagara; Terae, Satoshi; Shirato, Hiroki

doi:10.1016/j.jcct.2010.02.001

« Previous Next »Journal of Cardiovascular Computed Tomography
Volume 4, Issue 3 , Pages 218-220, May 2010

64-Slice MDCT imaging of endocardial cushion defect associated with other cardiac and extracardiac abnormalities

Noriko Oyama, MD, PhD
- Corresponding author.
- Department of Radiology, Hokkaido University Hospital, Kita 15, Nishi 7, Kita-ku, Sapporo 060-8638, Japan
Daisuke Goto, MD, PhD
- Department of Cardiovascular Medicine, Hokkaido University Graduate School of Medicine, Sapporo, Japan
Tsukasa Sasaki, RT
- Department of Radiology, Hokkaido University Hospital, Kita 15, Nishi 7, Kita-ku, Sapporo 060-8638, Japan
Hiroyuki Tsutsui, MD, PhD
- Department of Cardiovascular Medicine, Hokkaido University Graduate School of Medicine, Sapporo, Japan
Nagara Tamaki, MD, PhD
- Department of Nuclear Medicine, Hokkaido University Graduate School of Medicine, Sapporo, Japan
Satoshi Terae, MD, PhD
- Department of Radiology, Hokkaido University Hospital, Kita 15, Nishi 7, Kita-ku, Sapporo 060-8638, Japan
Hiroki Shirato, MD, PhD
- Department of Radiology, Hokkaido University Hospital, Kita 15, Nishi 7, Kita-ku, Sapporo 060-8638, Japan

Received 17 December 2009; accepted 14 February 2010. published online 22 February 2010.

Abstract

Electrocardiographic-gated 64-slice multidetector computed tomography (MDCT) was performed on a 30-year-old man who presented with a complete endocardial cushion defect (ECD) and severe pulmonary hypertension diagnosed when he was 3 years old. Multiplanar reconstruction image showed the common atrium without an atrial septum, a large ventricular septum defect, and a small right ventricle due to a complete atrioventricular canal defect. Three-dimensional CT volume-rending imaging showed a patent ductus arteriosus, dilation of the ascending aorta, and an anomalous-origin right coronary artery. This patient also had heterotaxy syndrome with polysplenia and azygos continuation. MDCT proved to be a good noninvasive imaging method for the evaluation of ECD associated with cardiac as well as extracardiac abnormalities.

Keywords: Congenital heart disease, Endocardial cushion defect, Heterotaxy syndrome, Multidetector computed tomography, Volume-rendering view